Essential amino acid for human development. Universal translation start signal although usually missing from mature protein. Isoln from casein: J. H. Mueller, Proc. Soc. Exp. Biol. Med. 19, 161 (1922). Early chemistry and biochemistry: Amino Acids and Proteins, D. M. Greenberg, Ed. (Charles C. Thomas, Springfield, IL, 1951) 950 pp., passim; J. P. Greenstein, M. Winitz, Chemistry of the Amino Acids vols. 1-3 (John Wiley and Sons, Inc., New York, 1961) pp. 2125-2155, passim. Determn and distribution in non-protein fractions: J. Giovanelli, S. H. Mudd, J. Biochem. Biophys. Methods 11, 1 (1985). GC-MS determn in biological fluids: S. P. Stabler et al., Anal. Biochem. 162, 185 (1987). Evaluation as tracer in cancer imaging in mice: R. Kubota, J. Nucl. Med. 36, 484 (1995). Clinical evaluation in acetaminophen overdose: A. N. Hamlyn et al., J. Int. Med. Res. 9, 226 (1981). Clinical use as radiolabel in hyperparathyroidism: P. Hellman et al., Surgery 116, 974 (1994). Review of metabolism and clinical significance in man: L. D. Fleisher, G. E. Gaull, Clin. Endocrinol. Metab. 3, 37-55 (1974); and in carcinogenesis: T. L. Gatton-Umphress, Hosp. Pract. 28, 83-90 (1993). Review of toxicity: N. J. Benevenga, J. Agric. Food Chem. 22, 2-9 (1974). Review of biosynthesis: I. G. Old et al., Prog. Biophys. Mol. Biol. 56, 145-185 (1991). Review as translation start signal: T. Meinnel et al., Biochimie 75, 1061-1075 (1993).
Converted by deamination, followed by transamination with resultant inversion to the l-form. Comparative study with l-form of metabolism in plants: M. Pokorny et al., Phytochemistry 9, 2175 (1970). Evaluation in parenteral nutrition: K J. Printen et al., Am. J. Clin. Nutr. 32, 1200 (1979). Review: L. D. Stegink, d-Amino Acids in Clin. Nutr. Update: Amino Acids H. L. Greene et al., Eds. (American Medical Association, Chicago, IL, 1977) pp 198-206.
Hepatoprotectant; antidote (acetaminophen poisoning); urinary acidifier.
Antidote (Acetaminophen Poisoning); Hepatoprotectant; Acidifier