Non-essential amino acid for human development but is required intermediate in arginine biosynthesis. Found in virtually all vertebrate tissues as well as incorporated into proteins, such as tyrocidine, q.v. Isolation from chicken excreta: M. Jaffe, Ber. 10, 1925 (1877). Early chemistry and biochemistry: J. P. Greenstein, M. Winitz, Chemistry of the Amino Acids (John Wiley and Sons, Inc., New York, 1961) pp. 2477-2491, passim. Review of synthesis: R. Yoshida, Synth. Prod. Util. Amino Acids, T. Kaneko et al., Eds (Kodansha Ltd, Tokyo, Japan, 1974) pp 166-170; of biosynthesis in plants: P. D. Shargool et al., Phytochemistry 27, 1571-1574 (1988). Brief historical review: H. A. Akers, E. V. Dromgoole, Trends Biochem. Sci. 7, 156-157 (1982). Review of metabolism: V. E. Shih, Enzyme 26, 254-258 (1981); of role in CNS functions: N. Seiler, G. Daune-Anglard, Metab. Brain Dis. 8, 151-179 (1993).
In treatment of hyperammonemia.